Imran Abid, Sajjad Ahmed, Tahir Naveed, Fatima Hamdani.
Arrhythmogenic right ventricular dysplasia with biventricular dysfunction confirmed by gated multi detector computerized tomography scan.
J Cardiovascular Dis Jan ;11(1):23-5.

Arrhythmogenic right ventricular dysplasia (ARVD) is a familial cardiomyopathy characterized by fibro fatty replacement of right ventricle. Frank left ventricular dysfunction is a rare occurrence in ARVD. Diagnosis is confirmed by magnetic resonance imaging (CMR) and /or biopsy but both are limited by logistic and technical factors. Multi detector computerized tomography (MDCT) scan is a useful and readily available non-invasive diagnostic alternative of CMR. We report a case of ARVD presenting with ventricular tachycardia (VT) and severe biventricular dysfunction confirmed by MDCT.

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