Nabeela Ata, Samee Akhtar.
Ehlers Danlos Syndrome with Pregnancy.
Gomal J Med Sci Jan ;3(2):69-70.

A 32 years old lady, G5 P0 A4 was admitted with gestational amenorrhoea of 20 weeks with the history of fall on the same day, as an emergency case. She was fully conscious when received and her vitals were stable, except the increased respiratory rate. Abdomen was soft, consistent with the period of gestation, no marks of external injury were noted on the body, except 3 bruises over her arm and forearms. Sonographic finding showed single active fetus of 20 weeks of fetal biometery. There was an episode of bleeding vaginally, which was mild. She had been seen by cardiologist for increased respiratory rate. After thorough history and examination, she was diagnosed as a case of Ehlers Danlos syndrome, on the basis of hypermobile joints, high arched palate, bruises due to fragile blood vessels, proximal muscle weakness. The final management plan was termination of pregnancy was planned after counseling the patient. She did not start any uterine contraction, it was repeated again and after the failure of establishment of uterine contraction, her caesarean section was planned. She delivered a baby girl of 0/10 A/S weighing 1.5 kg. Bilateral tubal ligation was performed. She did well in her postoperative period, except some shortness of breath which resolved spontaneously.

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